Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome

  • Srijana Bhandari Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Ganesh Dangal Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Aruna Karki Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Hema Pradhan Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Ranjana Shrestha Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Kabin Bhattachan Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Kenusha Devi Tiwari Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Sonu Bharati Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal
  • Sunita Maharjan Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal

Abstract

Mayer-Rokitansky-Kuster-Hauser syndrome also known as mullerian agenesis is a rare congenital condition in which there is absence of uterus along with upper vagina. Patient usually presents with primary amenorrhea with or without cyclical lower abdominal pain but have normal secondary sexual characters. Modified McIndoe Vaginoplasty with amnion graft is the commonest surgery performed worldwide. A 23 year old girl with normal secondary sexual characters presented with primary amenorrhea with cyclical lower abdominal pain; on examination blind vagina was present. Vaginoplasty with amnion graft was done and vaginal mould was placed. Vaginal dilatation with Hegar’s dilator was done weekly until 6 weeks. She is under regular follow-up at present and advised for regular manual dilation at home. McIndoe Vaginoplasty with amnion graft is a simple yet rewarding procedure especially in low resource countries like ours, with good success rate and with minimal postoperative complications.
Keywords: Amnion graft; Mayer-Rokitansky-Kuster-Hauser Syndrome; Modified McIndoe Vaginoplasty; Primary amenorrhea; Secondary sexual characters.

Published
2024-03-22
How to Cite
BhandariS., DangalG., KarkiA., PradhanH., ShresthaR., BhattachanK., TiwariK. D., BharatiS., & MaharjanS. (2024). Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome. Journal of Nepal Health Research Council, 21(3), 530-533. https://doi.org/10.33314/jnhrc.v21i3.4573